Cardiomyopathy

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cardiomyopathy

[¦kärd·ē·ō‚mī′äp·ə·thē]
(medicine)

Cardiomyopathy

 

(myocardosis), a term often applied to a broad group of heart diseases; specifically, noninflammatory lesions of the heart muscle (myocardium) resulting from a disturbance in myocardial metabolism. Among the causes of cardiomyopathy are nutritional disorders (alimentary dystrophy and avitaminosis, for example); protein metabolism disorders in hepatic or renal insufficiency and podagra; disturbances of carbohydrate metabolism (diabetes mellitus) and electrolyte metabolism; and endocrine disorders such as those associated with thyrotoxicosis and with hypoxia in impairment of coronary circulation, anemia, and mountain sickness. Myocardosis may also be caused by overstraining the myocardium and by exogenous poisons, such as carbon monoxide and alcohol.

In many cases the patient has no specific symptoms in the early stages; however, there may be shortness of breath and disagreeable sensations in the heart. Cardiomyopathy is manifested by dull, distant heart sounds, electrocardiographic changes, systolic murmur, extrasystole, and, more rarely, other types of arrhythmia. Severe cardiomyopathy weakens the heart contractions and may cause cardiac insufficiency. The changes associated with cardiomyopathy are usually reversible and disappear with the elimination of the underlying disease.

The cure includes treatment of the underlying disease and administration of agents that improve metabolic processes in the myocardium.

REFERENCE

Kedrov, A. A. Bolezni myshtsy serdtsa. Leningrad, 1963.

N. R. PALEEV

References in periodicals archive ?
Usefulness of immunostaining for plakoglobin as a diagnostic marker of arrhythmogenic right ventricular cardiomyopathy.
Four separate and distinct conditions of cardiomyopathy have been recognised: Arrhythmogenic Right Ventricular Cardiomyopathy (ARVC) is an electrical disturbance of the heart which tends to affect the right ventricle.
A postmortem examination revealed the teenager unknowingly had Arrhythmogenic Right Ventricular Cardiomyopathy, when the heart muscle changes into fat and stops it beating properly.
Arrhythmogenic right ventricular cardiomyopathy (ARVC) is characterized by progressive fatty or fibrofatty infiltration of the right ventricular myocardium, which constitutes a substrate for electrical instability and a focus of ventricular arrhythmias (1).
The second most common cause of unexpected sudden death in the young is Arrhythmogenic Right Ventricular Cardiomyopathy (ARVC), where the normal right ventricular muscle cells are replaced by fibrous tissue and fat.
There are four known separate and distinct conditions of cardiomyopathy - arrhythmogenic right ventricular cardiomyopathy, dilated cardiomyopathy, hypertrophic cardiomyopathy and restrictive cardiomyopathy.
Cardiomyopathies are progressive diseases that affect the heart muscle including Hypertrophic Cardiomyopathy (HCM), Dilated Cardiomyopathy (DCM), Conduction Disease associated with DCM (CD-DCM), and Arrhythmogenic Right Ventricular Cardiomyopathy (ARVC).
The FAMILION tests detect genetic mutations that can cause cardiac channelopathies or cardiomyopathies such as Long QT Syndrome (LQTS), Brugada Syndrome (BrS), Catecholaminergic Polymorphic Ventricular Tachycardia (CPVT), Hypertrophic Cardiomyopathy (HCM), and Arrhythmogenic Right Ventricular Cardiomyopathy (ARVC) in individuals and their families.

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