Creutzfeldt-Jakob disease

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Related to Creutzfeldt-Jakob disease: Huntington's disease, mad cow disease

Creutzfeldt-Jakob disease:

see prionprion
, abnormal form of a protein found in mammals, believed to cause a group of diseases known as

prion diseases or transmissible spongiform encephalopathies.
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References in periodicals archive ?
Iatrogenic Creutzfeldt-Jakob disease 22 years after human growth hormone therapy: clinical and radiological features.
And while scientists haven't been able to prove it yet, many believe that Stephen Churchill and the other victims in Great Britain may have gotten the variant form of Creutzfeldt-Jakob Disease after they ate meat from the tainted cows.
The Heidenhain variant of Creutzfeldt-Jakob disease.
A ban on blood donors who may have been exposed to the pathogen responsible for Creutzfeldt-Jakob disease (CJD) is expected to result in a critical blood shortage in Australia in December, when the new law is enforced.
And Government scientists warned of a link between BSE and Creutzfeldt-Jakob Disease in humans in 1989.
The Oprah show aired on April 16, 1996, less than a month after the British government reversed a decade of denial and admitted that consumption of beef from mad cows was the "most likely" explanation for the appearance of a bizarre, previously unseen dementia in humans known as "new variant Creutzfeldt-Jakob Disease," an incurable and invariably fatal strain that kills its victims by filling their brains with microscopic, spongy holes.
Panic followed the British government's announcement last year of a tentative link between mad cow disease and an untreatable and incurable human version of an ailment known as Creutzfeldt-Jakob disease, which occurs in about one in 1 million people in the world.
Specifically, Talecris has demonstrated that potential infection risk from pathogenic prions, including those associated with variant Creutzfeldt-Jakob Disease (vCJD, the human form of "Mad Cow") is significantly reduced during the manufacturing process in the unlikely event such prions are present in the plasma starting material.
Monitoring the occurrence of emerging forms of Creutzfeldt-Jakob disease in the United States.
Researchers have found that prions are responsible for similar diseases in several species: for example, Creutzfeldt-Jakob disease in people; bovine spongiform encephalopathy, also known as mad cow disease, in cows; and chronic wasting disease (CWD) in deer and elk.
At present, the only way to test for mad cow disease of the human equivalent -- Creutzfeldt-Jakob Disease -- is to examine the brain postmortem.