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von Gierke's disease
(redirected from Glycogen storage disease type I)

   Also found in: Medical, Wikipedia 0.01 sec.
von Gierke's disease [fȯn ′gir·kēz di‚zēz]
(medicine)
A form of glycogenosis characterized by marked diminution in or absence of hepatic glucose-6-phosphatase, resulting in hepatic glycogenosis, hypoglycemia, and acidosis. Also known as glycogen storage disease; hepatic glycogenosis; type I of Cori; van Crevald-von Gierke's disease.


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