Abbreviations AA: Amino acid AA-MF: Amino acid medical foods AI: Adequate intake AMDR: Acceptable macronutrient distribution ranges BMD: Bone mineral density BMI: Body mass index DGA: Dietary Guidelines for Americans DHA: Docosahexaenoic acid DRI: Dietary Reference Intake EAR: Estimated average requirements EPA: Eicosapentaenoic acid GMP-MF: Glycomacropeptide medical foods MF: Medical foods MLPF: Modified low-protein food MMA: Methylmalonic acid PAH: Phenylalanine hydroxylase PE: Protein equivalent RD: Registered dietitian UL: Tolerable upper intake level.
Median and percentile nutrient intakes AA-MF 10th Median 90th Energy, kcal/d 73 211 463 Protein, g/d 0.1 0.6 1.3 Phe, mg/d 3 13 60 Carbohydrate, 17 51 103 g/d Fiber, g/d 0 0.3 5 Fat, g/d 0 1 5 Saturated fat, 0 0.2 2 g/d Median and percentile nutrient intakes GMP-MF P 10th Median 90th Energy, kcal/d 85 257 690 0.31 Protein, g/d 0.2 0.4 1.6 0.71 Phe, mg/d 3 20 93 0.32 Carbohydrate, 14 62 125 0.49 g/d ([double dagger]) Fiber, g/d 0 1 6 0.13 Fat, g/d 0.5 3 18 0.13 ([double dagger]) Saturated fat, 0 0.5 4 0.25 g/d ([double dagger]) (1) Nutrient intakes from MLPF were based on 3-day food records (n = 13; classical PKU, n = 10; variant PKU, n = 3).