Malignant peripheral nerve sheath tumours as seen in our patient are among the least common variants with only 4 cases reported so far [6,13].
of Cases Swelling 33 Pain 11 Trauma 3 Recurrence 1 Table 3: Incidence of anatomic sites in soft tissue sarcomas Author Lower Extremity Upper Extremity Head and Neck Potter et al (4) 152(49.5%) 59(19.2%) 12(3.9%) Buhari et al (5) 80(41.6%) 19(9.8%) 27(14%) Present study 18(51.42%) 9(25.71%) 1(2.8%) Author Trunk Retroperitoneum Total Potter et al (4) 48(15.6%) 36(11.7%) 307 Buhari et al (5) 61(31.7%) 5(2.6%) 192 Present study 4(11.42%) 2(5.7%) 35 Table 4:
Malignant Peripheral Nerve Sheath Tumour as compared with that of Gabhane et al (10) and Nthumba et al (11) Tumour Gabhane et al (n=8) Nthumba et al (n=31) Characteristics (10) (11) Location in 1.
Smith et al., "[18F]2-fluoro-2-deoxy-D-glucose positron emission tomography (FDG PET) as a diagnostic tool for neurofibromatosis 1 (NF1) associated
malignant peripheral nerve sheath tumours (MPNSTs): a long-term clinical study," Annals of Oncology, vol.
{3} In this article we describe a case of low grade
malignant peripheral nerve sheath tumour of the paranasal sinuses, and we review the literature, clinical presentation, management, histopathology and prognosis of this tumour.
Multiple brain metastases from
malignant peripheral nerve sheath tumour (MPNST).
Moran, "
Malignant peripheral nerve sheath tumours in neurofibromatosis," Journal of Medical Genetics, vol.