fibromatosis

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fibromatosis

[¦fī·brō·mə′tō·səs]
(medicine)
The occurrence of multiple fibromas.
Localized proliferation of fibroblasts without apparent cause.
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References in periodicals archive ?
Several theories have been put forth regarding the formation of aggressive fibromatosis tumors.
Diagnosis of aggressive fibromatosis tumors is assisted by computed tomography (CT) scans and/ or MRI; core needle or open biopsy offers histologic confirmation.
1,2,8) Aggressive fibromatosis should be treated technically as a local malignancy, and a negative margin resection should be the operative goal.
Park et al describe excellent outcomes after administering radiation to patients with aggressive fibromatosis in the presence of gross or microscopic residual disease margins.
Desmoid tumors such as aggressive fibromatosis are notorious for recurring despite successful resection, with most authors reporting a recurrence rate ranging between 25 and 85% for extra-abdominal tumors.
In the past, aggressive fibromatosis has been known as juvenile fibromatosis, desmoplastic fibromatosis, extra-abdominal desmoid, and congenital fibrosarcoma.
Only two cases of aggressive fibromatosis involving the parapharyngeal space have been previously reported.
According to the World Health Organization's (WHO) classification of fibrous soft-tissue tumors, aggressive fibromatosis falls between benign and malignant neoplasms (table).
The first report of aggressive fibromatosis was published by MacFarlane in 1832.
On gross examination, aggressive fibromatosis is white to gray and has infiltrative margins.
12) A relationship also exists between aggressive fibromatosis and Gardner's syndrome; patients with Gardner's syndrome can also exhibit multiple desmoid tumors.
There have been no reports of malignant degeneration of aggressive fibromatosis after radiation therapy.

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