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Erythroderma
(redirected from congenital ichthyosiform erythroderma)

   Also found in: Dictionary/thesaurus, Medical, Acronyms, Wikipedia 0.01 sec.
Erythroderma 

the name for any of a group of diseases of humans manifested chiefly by an inflammatory reaction of the entire skin, including redness, edema, scaling, and itching. Primary erythrodermas occur as disease entities, for example, Ritter’s disease. Secondary erythrodermas develop along with existing skin diseases, such as eczema and psoriasis, or systemic diseases, for example, mycosis fungoides and blood diseases. The course of an erythroderma may be acute, subacute, or chronic.

Treatment is determined by the main cause. Desensitizing agents (calcium chloride, sodium thiosulfate) and antihistaminics (diphenyinhydramine hydrochloride, chloropyramine) are prescribed. Dietary restrictions are necessary.

REFERENCE

Mnogotomnoe rukovodstvo po dermato-venerologii, vol. 3. Moscow, 1964.


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Congenital ichthyosiform erythroderma is one of the severe ichthyoses for which no therapy is commercially available.
 
 
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congenital hypoplastic anemia
congenital hypoplastic anemia
congenital hypoplastic anemia
congenital hypothyroid dysmaturity syndrome
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Congenital hypotonia
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congenital hypotrichosis
congenital hypotrichosis universalis
congenital ichthyosiform erythroderma
Congenital ichthyosis
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congenital immunity
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congenital jaundice
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congenital joint disease
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