hydranencephaly


Also found in: Medical, Wikipedia.

hydranencephaly

[¦hī·drə‚en′sef·ə·lē]
(medicine)
A congenital anomaly in which there are vestiges of a cerebellum, occipital lobes, and basal nuclei; frontal and parietal lobes are replaced by a cyst; and the neurocranium is undeveloped.
References in periodicals archive ?
calves 2 4 Method of death Euthanasia 2 3 Spontaneous 0 1 Bodyweight, kg 49 [+ or -] 4 39 [+ or -] 3 ([double dagger]) ([section]) Axial musculoskeletal system Defect location Cervical 0 2 Thoracic 0 0 Lumbar 0 0 Type of deviation Lateral 0 2 Dorso-ventral 0 0 Helicoidal 0 0 Appendicular musculo-skeletal system Arthrogryposis 0 3 ([greater than or equal to]1 limb involved) Symetric limb NA 3 involvement Forelimb/hind limb NA 0 involvement Forelimbs only NA 2 Hind limbs only NA 1 Head Coaptation defect Prognathism 0 0 Brachygnathism 0 1 Altered profile Horse-like 0 1 Pig-like 0 0 Broken sagittal axis 0 1 Central nervous system Porencephaly 2 3 Hydranencephaly 1 1 Hydrocephaly 0 0 Cerebellar hypoplasia 0 0 Micromyelia 2 4 Characteristic WBD-2 WBD-3 ([dagger]) ([dagger]) No.
1) Cerebral damage can be severe, as cases of hydranencephaly with arterial and venous malformations have been reported.
When severe, hydrocephalus may be difficult to differentiate from hydranencephaly, which is an extreme form of cerebral encephalomalacia, probably the result of occlusion of both internal carotid arteries and infarction of all cerebral tissue (Figure 10).
In this rare condition, called hydranencephaly, cerebrospinal fluid fills the gaping hole within the child's head.
No normal cerebral tissue was seen, and hydranencephaly was suspected (Fig.
But Rachel, who suffers from a rare condition called hydranencephaly, has survived against all the odds and will celebrate her seventh birthday next month.
And given the apparent misdiagnosis of some infants with hydranencephaly, it is at least plausible that some might have a life worth living, albeit a profoundly limited one.
Hannah Hicks, whose daughter Alice was born with hydranencephaly - a central nervous disorder - said: "It's really nice to give something back after all they've done for us.
Among the 8 small ruminants that were SBV positive by ISH, hydrocephalus was found in 5, cerebellar hypoplasia in 5, hydranencephaly in 1, and arthrogryposis in 6.
The main behavioral difference described between normal newborns and those without cerebral hemispheres, whether due to anencephaly or hydranencephaly (in utero destruction of both cerebral hemispheres, with intact skull and scalp), is increased irritability and lack of habituation to repeated stimuli, [32] although even these differences are not universally observed among infants lacking forebrains.