von Gierke's disease
Also found in: Medical.
von Gierke's disease[fȯn ′gir·kēz di‚zēz]
A form of glycogenosis characterized by marked diminution in or absence of hepatic glucose-6-phosphatase, resulting in hepatic glycogenosis, hypoglycemia, and acidosis. Also known as glycogen storage disease; hepatic glycogenosis; type I of Cori; van Crevald-von Gierke's disease.