Beckwith-Wiedemann syndrome

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Beckwith-Wiedemann syndrome

[¦bek‚with ′wēd·ə·män ‚sin‚drōm]
(medicine)
A congenital, generalized overgrowth syndrome attributed to a relative deficiency of maternally derived genes that is characterized by visceromegaly and predisposition to childhood tumors, especially Wilms' tumor.
References in periodicals archive ?
This pediatric renal tumor (also called Wilms tumor or nephroblastoma) can be associated with numerous congenital anomalies which can occur as isolated entities or within well-defined syndromes (Beckwith Wiedemann, Denys-Drash, Perlman, Simpson-Golabi-Behmel, and WAGR syndromes) [20-27].
Significant changes in the chromosomal region 11p15 are reported to be associated with Beckwith Wiedemann syndrome, fetal over growth, or Silver-Russell syndrome (SRS) under growth (15).