For this reason, autosomal dominant PKD is often called "adult polycystic kidney disease
." Yet, in some cases, cysts may form earlier, even in the first years of life.
Adult polycystic kidney disease is an important cause of secondary hypertension in the children and in adults.
Adult polycystic kidney disease affects about 12.5 million people worldwide.
Epidemiology of adult polycystic kidney disease
. Am J Kidney Dis 1983;2:630-9.
A 38-year-old man with a 20-year history of adult polycystic kidney disease
and cysts in the liver presented with recurrent abdominal pain and progressive left flank discomfort.
Among total nephrectomies, 4(3.77%) benign neoplastic lesions were encountered, among which 2(1.84%) cases were oncocytoma, 1(0.94%) each were of multicystic nephroma & adult polycystic kidney disease
. Among 20(18.87%) cases of malignant neoplastic lesions, 12(11.32%) were renal cell carcinoma, 5(4.72%) were Wilm's tumor, 1(0.94%) case each of clear cell sarcoma kidney, congenital mesoblastic nephroma & transitional cell carcinoma.