agammaglobulinemia


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Related to agammaglobulinemia: hypogammaglobulinemia, Swiss type agammaglobulinemia

agammaglobulinemia

[ā‚gam·ə′gläb·yə·lən·ē·mē·ə]
(medicine)
The condition characterized by lack of or extremely low levels of gamma globulin in the blood, together with defective antibody production and frequent infections; primary agammaglobulinemia occurs in three clinical forms: congenital, acquired, and transient.
References in periodicals archive ?
Persistent and fatal central-nervous-system ECHOvirus infections in patients with agammaglobulinemia.
Drug reaction to ceftriaksone in a child with X-linked agammaglobulinemia.
Sepsis caused by Veillonella parvula infection in a 17-year old patient with X-linked agammaglobulinemia.
HIV infection, systemic lupus erythematosus, lymphoproliferative disorders, myelodysplasia, agammaglobulinemia or hypogammaglobulinemia, drug-induced thrombocytopenia, alloimmune thrombocytopenia, congenital hereditary nonimmune thrombocytopenia) .
CVID is partially a diagnosis of exclusion, in that other primary antibody deficiencies such as X-linked agammaglobulinemia and hyperimmunoglobulin M syndrome must not be present.
Among the possible treatments are the elimination of chronic sinusitis, avoidance of or desensitization to offending allergens, repair of a cleft palate, treatment of agammaglobulinemia, or tonsillectomy and adenoidectomy.
David contracted VAPP when he was five-months old and remained undiagnosed for two years, when it was also found that he had Brutons agammaglobulinemia, a rare genetic disorder, which causes immune deficiency.
This includes, but is not limited to, common variable immunodeficiency (CVID), X-linked agammaglobulinemia, congenital agammaglobulinemia, Wiskott-Aldrich syndrome, and severe combined immunodeficiencies.
This includes, but is not limited to, the humoral immune defect in common variable immunodeficiency (CVID), X-linked agammaglobulinemia, congenital agammaglobulinemia, Wiskott-Aldrich syndrome, and severe combined immunodeficiencies.