European Society for Immunodeficiencies Diagnostic Criteria for Common Variable Immunodeficiency
Espanol, "Common variable immunodeficiency
: 20-yr experience at a single centre," Pediatric Allergy and Immunology, vol.
Diagnostic findings in 95 Finnish patients with common variable immunodeficiency
. J Clin Immunol 2001; 21:145-9.
B-cell antibody defects account for around 50% of them, selective IgA deficiency being the most common, followed by common variable immunodeficiency
Lymphomas of mucosa-associated lymphoid tissue in common variable immunodeficiency
. Am J Hematol 2002;69:171-8.
Song et al., "Regulatory T cell dysfunction in subjects with common variable immunodeficiency
complicated by autoimmune disease," Clinical Immunology, vol.
Moin et al., "A single-center 20-year survey of infectious complication in 64 patients with common variable immunodeficiency
," Medical Journal of The Islamic Republic of Iran, vol.
Alvarez et al., "Immunoglobulin therapy to control lung damage in patients with common variable immunodeficiency
," International Immunopharmacology, vol.
Individual cases of chemical fume exposure, and cases associated with common variable immunodeficiency
and transplantation are singlecase reports and appear to be sporadic associations.
A woman in Minnesota aged 44 years with long-standing common variable immunodeficiency
died after developing VAPP in 2009 (4).
Autoimmune enteropathy is often found in patients with selective IgA deficiency, common variable immunodeficiency
(CVID) and IPEX,3,4 but the role of NK cells remains undetermined.6,7 In our case report, patient initially presented with CD which was difficult to manage along with recurrent, opportunistic infections such as candidiasis and CMV disease.