Skin biopsy from follicular papules revealed hyperkeratosis and papillomatosis of epidermis with mild chronic inflammatory infiltrate in dermis as shown in Figure 3.
Pachyonychia congenita is a rare type of palmoplantar keratoderma characterized by a triad of subungual hyperkeratosis, keratosis palmaris et plantaris and oral mucosal leukokeratosis.6 It is associated with other features like hyperkeratotic follicular papules, keratosis pilaris, hyperhidrosis of palms and soles, and hair abnormalities.
It is clinically characterized by a triad of cicatricial alopecia of scalp, axillary and pubic hypotrichosis of nonscarring type and keratotic follicular papules
over body consistent with follicular LP.2 LPP causing cicatricial alopecia may be classic LPP, frontal fibrosing alopecia (FFP) or fibrosing alopecia in a patterned distribution (FADP).13,14 In our patient hair loss was consistent with FFA and FAPD.
The follicular papules are usually found on toddlers or infants who are especially "squirmy" and constantly uncomfortable.
"We see this patch of follicular papules quite often at Howard," Dr.
Phrynoderma occurs usually in children and adolescents and is characterized by hyperkeratotic, follicular papules with keratotic plug distributed over elbows, knees, extensor extremities and buttocks, though any part of the body may be involved.
DISCUSSION: Hyperkeratotic follicular papules are seen in many other dermatological disorders and mild degree of follicular prominence may be seen during winter season, especially in children.
or pustules, often in irregularly linear groups, develop on the nape of the neck just below the hair line.
Since then she has been almost devoid of scalp hair, eyebrows and eye lashes (figure.2) Follicular papules on the scalp started appearing in the 1st year.
DISCUSSION: APL is an autosomal recessive form of total alopecia, characterized by hair loss soon after birth and the development of follicular papules with absence of terminal hair growth.