Other entities in the differential diagnosis include Wilm's tumor, hepatoblastoma, solid and cystic papillary tumor of the pancreas, non-Hodgkin lymphoma, and a Kaposiform hemangioendothelioma
Hannah, now 19 months, suffers from Kaposiform hemangioendothelioma
with Kasabach-Merritt syndrome - which means tumours make platelet level drop dangerously low.
The histologic differential diagnosis of KS includes other vascular tumors such as benign lymphangioendothelioma, hobnail hemangioma, spindle cell hemangioma, kaposiform hemangioendothelioma, cutaneous angiosarcoma, and acroangiodermatitis.
D2-40 immunohistochemical analysis of pediatric vascular tumors reveals positivity in kaposiform hemangioendothelioma.
Tumors Juvenile hemangioma Rapidly involuting congenital hemangioma Noninvoluting congenital hemangioma Kaposiform hemangioendothelioma
Tufted angioma * Vascular malformations High-flow Arteriovenous malformation Low-flow Venous malformation Lymphatic malformation Lymphatic-venous malformation Capillary (or venular) malformation (portwine stain)
Kaposiform hemangioendothelioma is an uncommon vascular neoplasm initially described in 1979 as a congenital retroperitoneal hemangioendothelioma.
3-7] Several retrospective studies on patients who presented with Kasabach-Merritt syndrome have revealed that what was originally diagnosed as a capillary hemangioma may often be better described as a Kaposiform hemangioendothelioma.
According to our review of the literature, the histopathology of Kaposiform hemangioendothelioma in the thymus has not been described previously.