We are reporting a rare variant of this syndrome having a complex congenital cardiac disease, including tricuspid atresia
, pulmonary stenosis, and atrial septal aneurysm in association with the usual ASD, VSD, and the structural skeletal defects along with an unusual presentation of stroke.
ANOMALIES Fused heart 01 Mesocardia 01 Dextrocardia with CORV 02 Interrupted aortic arch 02 Abnormal origin of right 01 subclavian artery Tetralogy of Fallot 01 V.S.D 07 A.S.D 01 Transposition of great vessels 01 Persistent truncus arteriosus 01 with tricuspid atresia
, elongated hypertrophied abnormally positioned Rt.
Distribution of the patients by diagnosis n % Diagnosis Transposition of the great arteries 28 33.7 Pulmonary atresia 16 19.3 Aortic coarctation 10 12.0 Single ventricle 6 7.2 Hypoplastic left heart syndrome 6 7.2 Tricuspid atresia
5 6.0 Pulmonary stenosis 3 3.6 Truncus arteriosus 2 2.4 Aortic arch anomaly 2 2.4 Cardiomyopathy 1 1.2 Taussig Bing anomaly 2 2.4 Valvular aortic stenosis 1 1.2 AV complete block 1 1.2 Total 83 100.0 Table 3.
The SACHDNC had identified seven specific lesions as primary targets for screening: hypoplastic left heart syndrome, pulmonary atresia, tetralogy of Fallot, total anomalous pulmonary venous return, transposition of the great arteries, tricuspid atresia
, and truncus arteriosus.
Jessica was born with only half a heart that works properly because of a rare congenital defect called Tricuspid Atresia
. It means, says mum Joanna Poulsen Jenkins, that her daughter has been to "hell and back".
Examples include tricuspid atresia
, pulmonary atresia/intact ventricular septum and hypoplastic left heart syndrome.
MICHAEL DUNN WAS BORN WITH TRICUSPID ATRESIA
. The Fontan procedure (consisting of three surgical procedures), was employed to correct the defect.
The daughter of Ryan and Kara Powers was born, like Isabelle, with myriad complications - hypoplastic right ventricle, transposition of the great arteries, aortic stenosis, tricuspid atresia
and atrial and ventricular septal defects.
Matthew was born with tricuspid atresia
, which means he has only one ventricle.
A 3-month old infant underwent left Blalock-Taussig and right Glenn shunting following earlier surgical repair of tricuspid atresia
. Due to lack of central venous access, a direct right atrial catheter was inserted at surgery for monitoring and to give parenteral nutrition of intralipid and glucose-amino acid solution.